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PART 16: Endocrinology and Metabolism
SECTION 3   Disorders of Intermediary Metabolism

364 Inherited Disorders of Amino Acid Metabolism in Adults
Nicola Longo

Figure 364-1  Pathways, enzymes, and coenzymes involved in the homocystinurias. Methionine transfers a methyl group during its conversion to homocysteine. Defects in methyl transfer or in the subsequent metabolism of homocysteine by the pyridoxal phosphate (vitamin B6)-dependent cystathionine b- ...
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