PART 16: Endocrinology and Metabolism
SECTION 3 Disorders of Intermediary Metabolism
364 Inherited Disorders of Amino Acid Metabolism in Adults
![]() | Figure 364-1 Pathways, enzymes, and coenzymes involved in the homocystinurias. Methionine transfers a methyl group during its conversion to homocysteine. Defects in methyl transfer or in the subsequent metabolism of homocysteine by the pyridoxal phosphate (vitamin B6)-dependent cystathionine b- ... |
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